hrp0086p1-p140 | Bone & Mineral Metabolism P1 | ESPE2016

Bone Mass and Vitamin D Status in Children and Adolescents with Generalized Epidermolysis Bullosa

Claudio Castro Luiz , Nobrega Yanna , Gandolfi Lenora , Pratesi Riccardo

Background: Inherited epidermolysis bullosa (EB) comprises a cluster of genetic disorders characterized by blistering of skin and mucosae following minimal mechanical traumas. Severely affected individuals have high risk of extracutaneous complications, including chronic undernourishment and low bone mass.Objective and hypotheses: The aims of this study were to assess the areal bone mineral density (aBMD) and vitamin D status of children and adolescents ...